Mahmood, Fahad

A zebrafish model of CLN2 disease is deficient in tripeptidyl peptidase 1 and displays progressive neurodegeneration accompanied by a reduction in proliferation. [electronic resource] - Brain : a journal of neurology May 2013 - 1488-507 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

1460-2156

10.1093/brain/awt043 doi


Aminopeptidases--deficiency
Animals
Animals, Genetically Modified
Cell Proliferation
Dipeptidyl-Peptidases and Tripeptidyl-Peptidases--deficiency
Disease Models, Animal
Disease Progression
Growth Inhibitors--deficiency
Humans
Motor Activity--physiology
Neurodegenerative Diseases--enzymology
Neuronal Ceroid-Lipofuscinoses--enzymology
Serine Proteases--deficiency
Tripeptidyl-Peptidase 1
Zebrafish