Hanada, Toshikatsu
CLP1 links tRNA metabolism to progressive motor-neuron loss. [electronic resource]
- Nature Mar 2013
- 474-80 p. digital
Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't
1476-4687
10.1038/nature11923 doi
Amyotrophic Lateral Sclerosis
Animals
Animals, Newborn
Axons--metabolism
Cell Death
Diaphragm--innervation
Embryo Loss
Embryo, Mammalian--metabolism
Exons--genetics
Female
Fibroblasts
Male
Mice
Mice, Inbred C57BL
Mice, Knockout
Mice, Transgenic
Motor Neurons--metabolism
Muscular Atrophy, Spinal
Neuromuscular Diseases--metabolism
Oxidative Stress
RNA Processing, Post-Transcriptional
RNA, Transfer, Tyr--genetics
RNA-Binding Proteins
Respiration
Spinal Nerves--cytology
Transcription Factors--deficiency
Tumor Suppressor Protein p53--metabolism
Tyrosine--genetics