Hanada, Toshikatsu

CLP1 links tRNA metabolism to progressive motor-neuron loss. [electronic resource] - Nature Mar 2013 - 474-80 p. digital

Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't

1476-4687

10.1038/nature11923 doi


Amyotrophic Lateral Sclerosis
Animals
Animals, Newborn
Axons--metabolism
Cell Death
Diaphragm--innervation
Embryo Loss
Embryo, Mammalian--metabolism
Exons--genetics
Female
Fibroblasts
Male
Mice
Mice, Inbred C57BL
Mice, Knockout
Mice, Transgenic
Motor Neurons--metabolism
Muscular Atrophy, Spinal
Neuromuscular Diseases--metabolism
Oxidative Stress
RNA Processing, Post-Transcriptional
RNA, Transfer, Tyr--genetics
RNA-Binding Proteins
Respiration
Spinal Nerves--cytology
Transcription Factors--deficiency
Tumor Suppressor Protein p53--metabolism
Tyrosine--genetics