Gain-of-function ADAMTS13 variants that are resistant to autoantibodies against ADAMTS13 in patients with acquired thrombotic thrombocytopenic purpura. [electronic resource]
- Blood Apr 2012
- 3836-43 p. digital
Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't
1528-0020
10.1182/blood-2011-12-399501 doi
ADAM Proteins--chemistry ADAMTS13 Protein Adult Aged Animals Antibody Specificity Autoantibodies--immunology Binding Sites, Antibody--immunology COS Cells Chlorocebus aethiops Female Genetic Variation Humans Immunoglobulin G--immunology Immunotherapy--methods Male Middle Aged Mutagenesis, Site-Directed Protein Structure, Tertiary Purpura, Thrombotic Thrombocytopenic--genetics Recombinant Proteins--chemistry Young Adult