Fuller, Maria

Mass spectrometric quantification of glycogen to assess primary substrate accumulation in the Pompe mouse. [electronic resource] - Analytical biochemistry Feb 2012 - 759-63 p. digital

Publication Type: Journal Article

1096-0309

10.1016/j.ab.2011.12.026 doi


Animals
Chromatography, Liquid
Disease Models, Animal
Glycogen--analysis
Glycogen Storage Disease Type II--metabolism
Mice
Mice, Knockout
Muscle, Skeletal--metabolism
Spectrometry, Mass, Electrospray Ionization--methods
alpha-Glucosidases--genetics