TY - GEN AU - Ma,Lijie AU - Liu,Yan AU - El-Achkar,Tarek M AU - Wu,Xue-Ru TI - Molecular and cellular effects of Tamm-Horsfall protein mutations and their rescue by chemical chaperones SN - 1083-351X PY - 2012///0227 KW - Animals KW - Apoptosis KW - genetics KW - Cell Line KW - Dogs KW - Endoplasmic Reticulum KW - Genetic Diseases, Inborn KW - HSP70 Heat-Shock Proteins KW - Humans KW - Kidney Diseases, Cystic KW - Mice KW - Mutation KW - Polycystic Kidney, Autosomal Dominant KW - Protein Folding KW - Protein Structure, Tertiary KW - Protein Transport KW - Uromodulin N1 - Publication Type: Journal Article; Research Support, N.I.H., Extramural UR - https://doi.org/10.1074/jbc.M111.283036 ER -