TY - GEN AU - Fischer,Lindsey R AU - Li,Yingjie AU - Asress,Seneshaw A AU - Jones,Dean P AU - Glass,Jonathan D TI - Absence of SOD1 leads to oxidative stress in peripheral nerve and causes a progressive distal motor axonopathy SN - 1090-2430 PY - 2012///0325 KW - Acetylcysteine KW - pharmacology KW - Age Factors KW - Analysis of Variance KW - Animals KW - Axons KW - pathology KW - Bacterial Proteins KW - genetics KW - Calcium-Binding Proteins KW - metabolism KW - Chromatography, High Pressure Liquid KW - DNA-Binding Proteins KW - Free Radical Scavengers KW - Glial Fibrillary Acidic Protein KW - Glutathione KW - Glutathione Disulfide KW - Luminescent Proteins KW - Mice KW - Mice, Knockout KW - Microfilament Proteins KW - Muscle Denervation KW - methods KW - Muscle, Skeletal KW - physiopathology KW - Nerve Fibers KW - Neuromuscular Junction KW - Oxidation-Reduction KW - drug effects KW - Oxidative Stress KW - Peripheral Nerves KW - Peripheral Nervous System Diseases KW - Presynaptic Terminals KW - Skin KW - innervation KW - Superoxide Dismutase KW - deficiency KW - Superoxide Dismutase-1 KW - Ubiquitin Thiolesterase KW - Ubiquitins N1 - Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't UR - https://doi.org/10.1016/j.expneurol.2011.09.020 ER -