Fischer, Lindsey R

Absence of SOD1 leads to oxidative stress in peripheral nerve and causes a progressive distal motor axonopathy. [electronic resource] - Experimental neurology Jan 2012 - 163-71 p. digital

Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't

1090-2430

10.1016/j.expneurol.2011.09.020 doi


Acetylcysteine--pharmacology
Age Factors
Analysis of Variance
Animals
Axons--pathology
Bacterial Proteins--genetics
Calcium-Binding Proteins--metabolism
Chromatography, High Pressure Liquid
DNA-Binding Proteins--metabolism
Free Radical Scavengers--pharmacology
Glial Fibrillary Acidic Protein--metabolism
Glutathione--metabolism
Glutathione Disulfide--metabolism
Luminescent Proteins--genetics
Mice
Mice, Knockout
Microfilament Proteins--metabolism
Muscle Denervation--methods
Muscle, Skeletal--physiopathology
Nerve Fibers--pathology
Neuromuscular Junction--physiopathology
Oxidation-Reduction--drug effects
Oxidative Stress--genetics
Peripheral Nerves--metabolism
Peripheral Nervous System Diseases--pathology
Presynaptic Terminals--metabolism
Skin--innervation
Superoxide Dismutase--deficiency
Superoxide Dismutase-1
Ubiquitin Thiolesterase--metabolism
Ubiquitins--metabolism