Fischer, Lindsey R
Absence of SOD1 leads to oxidative stress in peripheral nerve and causes a progressive distal motor axonopathy. [electronic resource]
- Experimental neurology Jan 2012
- 163-71 p. digital
Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't
ISSN: 1090-2430
Standard No.: 10.1016/j.expneurol.2011.09.020 doi
Subjects--Topical Terms: Acetylcysteine--pharmacology Age Factors Analysis of Variance Animals Axons--pathology Bacterial Proteins--genetics Calcium-Binding Proteins--metabolism Chromatography, High Pressure Liquid DNA-Binding Proteins--metabolism Free Radical Scavengers--pharmacology Glial Fibrillary Acidic Protein--metabolism Glutathione--metabolism Glutathione Disulfide--metabolism Luminescent Proteins--genetics Mice Mice, Knockout Microfilament Proteins--metabolism Muscle Denervation--methods Muscle, Skeletal--physiopathology Nerve Fibers--pathology Neuromuscular Junction--physiopathology Oxidation-Reduction--drug effects Oxidative Stress--genetics Peripheral Nerves--metabolism Peripheral Nervous System Diseases--pathology Presynaptic Terminals--metabolism Skin--innervation Superoxide Dismutase--deficiency Superoxide Dismutase-1 Ubiquitin Thiolesterase--metabolism Ubiquitins--metabolism