TY - GEN AU - Spencer,Carolyn T AU - Byrne,Barry J AU - Bryant,Randall M AU - Margossian,Renee AU - Maisenbacher,Melissa AU - Breitenger,Petar AU - Benni,Paul B AU - Redfearn,Sharon AU - Marcus,Edward AU - Cade,W Todd TI - Impaired cardiac reserve and severely diminished skeletal muscle O₂ utilization mediate exercise intolerance in Barth syndrome SN - 1522-1539 PY - 2011///1223 KW - Adolescent KW - Adrenergic beta-Antagonists KW - therapeutic use KW - Analysis of Variance KW - Barth Syndrome KW - complications KW - Biomarkers KW - blood KW - Blood Pressure KW - Cardiomyopathy, Dilated KW - diagnosis KW - Case-Control Studies KW - Child KW - Cross-Sectional Studies KW - Echocardiography KW - Electrocardiography KW - Exercise Test KW - Exercise Tolerance KW - Heart Rate KW - Hemoglobins KW - metabolism KW - Humans KW - Male KW - Muscle Contraction KW - Oxygen KW - Oxygen Consumption KW - Quadriceps Muscle KW - Respiratory Mechanics KW - Spectroscopy, Near-Infrared KW - Ventricular Function, Left KW - Young Adult N1 - Publication Type: Journal Article; Research Support, Non-U.S. Gov't UR - https://doi.org/10.1152/ajpheart.00479.2010 ER -