Visser, Gepke

Survival, but not maturation, is affected in neutrophil progenitors from GSD-1b patients. [electronic resource] - Journal of inherited metabolic disease Mar 2012 - 287-300 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

1573-2665

10.1007/s10545-011-9379-4 doi


Adolescent
Animals
Antiporters--deficiency
Apoptosis--genetics
Cell Differentiation--genetics
Child
Child, Preschool
Cytokines--blood
Female
Glucose--metabolism
Glycogen Storage Disease Type I--blood
Hematopoietic Stem Cells--metabolism
Homeostasis--genetics
Humans
Inflammatory Bowel Diseases--blood
Intestinal Mucosa--metabolism
Leukocytes, Mononuclear--metabolism
Male
Mesenchymal Stem Cells--metabolism
Mice
Mice, Inbred NOD
Mice, SCID
Monosaccharide Transport Proteins--deficiency
Neutropenia--blood
Neutrophils--metabolism
Survival Rate