Dale, Jeffrey M

The spinal muscular atrophy mouse model, SMAΔ7, displays altered axonal transport without global neurofilament alterations. [electronic resource] - Acta neuropathologica Sep 2011 - 331-41 p. digital

Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't

1432-0533

10.1007/s00401-011-0848-5 doi


Animals
Animals, Newborn
Axons--pathology
Biological Transport--genetics
Disease Models, Animal
Gene Expression Regulation--genetics
Humans
Membrane Glycoproteins--metabolism
Mice
Mice, Transgenic
Microscopy, Electron, Transmission--methods
Muscular Atrophy, Spinal--complications
Mutation--genetics
Nerve Tissue Proteins--metabolism
Neurofilament Proteins--genetics
Neuromuscular Junction--metabolism
SMN Complex Proteins--genetics
Sciatic Nerve--metabolism
Sciatic Neuropathy--metabolism
Synaptotagmins--metabolism