Askanas, Valerie
Sporadic inclusion-body myositis: conformational multifactorial ageing-related degenerative muscle disease associated with proteasomal and lysosomal inhibition, endoplasmic reticulum stress, and accumulation of amyloid-β42 oligomers and phosphorylated tau. [electronic resource]
- Presse medicale (Paris, France : 1983) Apr 2011
- e219-35 p. digital
Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't; Review
2213-0276
10.1016/j.lpm.2010.11.024 doi
Age Factors
Amyloid beta-Peptides--metabolism
Autophagy--physiology
Biopsy
Endoplasmic Reticulum--pathology
Humans
Lysosomes--metabolism
Microscopy, Electron
Muscle Fibers, Skeletal--pathology
Muscles--pathology
Myositis, Inclusion Body--pathology
Myostatin--metabolism
Peptide Fragments--metabolism
Phosphorylation
Proteasome Endopeptidase Complex--metabolism
Protein Conformation
Proteostasis Deficiencies--pathology
Sirtuin 1--metabolism
Ubiquitin-Protein Ligases--metabolism
alpha-Synuclein--metabolism
tau Proteins--metabolism