Ochala, Julien

Disrupted myosin cross-bridge cycling kinetics triggers muscle weakness in nebulin-related myopathy. [electronic resource] - FASEB journal : official publication of the Federation of American Societies for Experimental Biology Jun 2011 - 1903-13 p. digital

Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't

1530-6860

10.1096/fj.10-176727 doi


Adult
Gene Expression Regulation--physiology
Humans
Kinetics
Male
Middle Aged
Muscle Proteins--genetics
Muscle Weakness--genetics
Muscle, Skeletal--metabolism
Mutation
Myopathies, Nemaline--genetics
Myosins--chemistry
X-Ray Diffraction