Wajner, Moacir <br/><br/>
Disruption of mitochondrial homeostasis in organic acidurias: insights from human and animal studies.  [electronic resource] 

 -  Journal of bioenergetics and biomembranes  Feb 2011 
 - 31-8 p.  digital 
<br/><br/> Publication Type: Journal Article; Research Support, Non-U.S. Gov't; Review 
<br/><br/><label>ISSN: </label>1573-6881 
<br/><br/><label>Standard No.: </label>10.1007/s10863-011-9324-0  doi 
<br/><br/><label>Subjects--Topical Terms: </label><br/>Acetyl-CoA C-Acyltransferase--deficiency<br/>Adenosine Triphosphate--metabolism<br/>Amino Acid Metabolism, Inborn Errors--physiopathology<br/>Animals<br/>Barth Syndrome--physiopathology<br/>Brain Diseases, Metabolic--physiopathology<br/>Brain Diseases, Metabolic, Inborn--physiopathology<br/>Carboxylic Acids--metabolism<br/>Glutaryl-CoA Dehydrogenase--deficiency<br/>Homeostasis--physiology<br/>Humans<br/>Metabolism, Inborn Errors--physiopathology<br/>Mitochondria--metabolism<br/>Mitochondrial Diseases--physiopathology<br/>Propionic Acidemia--physiopathology<br/>Purpura--physiopathology