Schmidt, Stinne P

Toxic response caused by a misfolding variant of the mitochondrial protein short-chain acyl-CoA dehydrogenase. [electronic resource] - Journal of inherited metabolic disease Apr 2011 - 465-75 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

1573-2665

10.1007/s10545-010-9255-7 doi


Animals
Antioxidants--chemistry
Butyryl-CoA Dehydrogenase--chemistry
Cell Proliferation
Genetic Variation
Genotype
Humans
Mice
Mitochondrial Diseases--metabolism
Mitochondrial Proteins--chemistry
Oxidative Stress
Phenotype
Protein Denaturation
Protein Folding
Proteomics--methods