Wanders, Ronald J A <br/><br/>
Enzymology of the branched-chain amino acid oxidation disorders: the valine pathway.  [electronic resource] 

 -  Journal of inherited metabolic disease  Jan 2012 
 - 5-12 p.  digital 
<br/><br/> Publication Type: Journal Article 
<br/><br/><label>ISSN: </label>1573-2665 
<br/><br/><label>Standard No.: </label>10.1007/s10545-010-9236-x  doi 
<br/><br/><label>Subjects--Topical Terms: </label><br/>Amino Acid Metabolism, Inborn Errors--diagnosis<br/>Amino Acids, Branched-Chain--metabolism<br/>Animals<br/>Enoyl-CoA Hydratase--metabolism<br/>Humans<br/>Hydroxybutyrate Dehydrogenase--metabolism<br/>Methylmalonate-Semialdehyde Dehydrogenase (Acylating)--metabolism<br/>Mitochondria--metabolism<br/>Models, Chemical<br/>Oxidoreductases Acting on CH-CH Group Donors--metabolism<br/>Oxygen--chemistry<br/>Thiolester Hydrolases--metabolism<br/>Valine--chemistry