Grefhorst, Aldo

Carbohydrate-response-element-binding protein (ChREBP) and not the liver X receptor α (LXRα) mediates elevated hepatic lipogenic gene expression in a mouse model of glycogen storage disease type 1. [electronic resource] - The Biochemical journal Dec 2010 - 249-54 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

1470-8728

10.1042/BJ20101225 doi


Animals
Basic Helix-Loop-Helix Leucine Zipper Transcription Factors
Cholesterol--metabolism
Disease Models, Animal
Gene Expression Regulation
Glucose-6-Phosphatase--adverse effects
Glycogen Storage Disease--enzymology
Humans
Imidazoles--administration & dosage
Liver--enzymology
Liver Glycogen--metabolism
Liver X Receptors
Male
Mice
Mice, Inbred C57BL
Mice, Knockout
Nuclear Proteins--deficiency
Orphan Nuclear Receptors--deficiency
Pyridines--administration & dosage
RNA--genetics
Transcription Factors--deficiency
Triglycerides--metabolism