Regulatory insertion removal restores maturation, stability and function of DeltaF508 CFTR. [electronic resource]
- Journal of molecular biology Aug 2010
- 194-210 p. digital
Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't
1089-8638
10.1016/j.jmb.2010.06.019 doi
Adenosine Triphosphate--metabolism Animals Binding Sites--genetics Biological Transport, Active Cell Line Cell Membrane--metabolism Cricetinae Cystic Fibrosis--genetics Cystic Fibrosis Transmembrane Conductance Regulator--chemistry Humans In Vitro Techniques Mice Models, Molecular Molecular Dynamics Simulation Mutant Proteins--chemistry Protein Interaction Domains and Motifs Protein Processing, Post-Translational Protein Stability Recombinant Proteins--chemistry Sequence Deletion