TY - GEN AU - Maitra,Meenakshi AU - Wang,Yongyu AU - Gerard,Robert D AU - Mendelson,Carole R AU - Garcia,Christine Kim TI - Surfactant protein A2 mutations associated with pulmonary fibrosis lead to protein instability and endoplasmic reticulum stress SN - 1083-351X PY - 2010///0806 KW - Amino Acid Substitution KW - drug effects KW - Animals KW - Biomarkers KW - metabolism KW - Bronchoalveolar Lavage Fluid KW - chemistry KW - Cell Extracts KW - Cell Line, Tumor KW - Detergents KW - pharmacology KW - Dogs KW - Endoplasmic Reticulum KW - Female KW - Humans KW - Leupeptins KW - Male KW - Mutant Proteins KW - Mutation KW - genetics KW - Pedigree KW - Protein Processing, Post-Translational KW - Protein Stability KW - Protein Structure, Quaternary KW - Pulmonary Alveoli KW - Pulmonary Fibrosis KW - Pulmonary Surfactant-Associated Protein A KW - Solubility KW - Stress, Physiological N1 - Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't UR - https://doi.org/10.1074/jbc.M110.121467 ER -