Rauh, Robert

A mutation of the epithelial sodium channel associated with atypical cystic fibrosis increases channel open probability and reduces Na+ self inhibition. [electronic resource] - The Journal of physiology Apr 2010 - 1211-25 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

1469-7793

10.1113/jphysiol.2009.180224 doi


Animals
Cells, Cultured
Chymotrypsin--metabolism
Cystic Fibrosis--physiopathology
Cystic Fibrosis Transmembrane Conductance Regulator--genetics
Epithelial Sodium Channels--genetics
Feedback, Physiological--physiology
Female
Humans
Mutation--genetics
Oocytes--cytology
Patch-Clamp Techniques
Phenotype
Plasmids
Sodium--metabolism
Xenopus laevis