TY - GEN AU - Lemaire,Raphael AU - Farina,Giuseppina AU - Bayle,Julie AU - Dimarzio,Michael AU - Pendergrass,Sarah A AU - Milano,Ausra AU - Perbal,Bernard AU - Whitfield,Michael L AU - Lafyatis,Robert TI - Antagonistic effect of the matricellular signaling protein CCN3 on TGF-beta- and Wnt-mediated fibrillinogenesis in systemic sclerosis and Marfan syndrome SN - 1523-1747 PY - 2010///0615 KW - Animals KW - Biopsy KW - CCN Intercellular Signaling Proteins KW - Case-Control Studies KW - Cells, Cultured KW - Disease Models, Animal KW - Fibrillin-1 KW - Fibrillins KW - Humans KW - Intracellular Signaling Peptides and Proteins KW - metabolism KW - Marfan Syndrome KW - Mice KW - Mice, Mutant Strains KW - Microfilament Proteins KW - antagonists & inhibitors KW - Nephroblastoma Overexpressed Protein KW - Proto-Oncogene Proteins KW - Scleroderma, Systemic KW - Signal Transduction KW - physiology KW - Skin KW - Smad3 Protein KW - Transforming Growth Factor beta KW - Wnt Proteins N1 - Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't UR - https://doi.org/10.1038/jid.2010.15 ER -