Lemaire, Raphael <br/><br/>
Antagonistic effect of the matricellular signaling protein CCN3 on TGF-beta- and Wnt-mediated fibrillinogenesis in systemic sclerosis and Marfan syndrome.  [electronic resource] 

 -  The Journal of investigative dermatology  Jun 2010 
 - 1514-23 p.  digital 
<br/><br/> Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't 
<br/><br/><label>ISSN: </label>1523-1747 
<br/><br/><label>Standard No.: </label>10.1038/jid.2010.15  doi 
<br/><br/><label>Subjects--Topical Terms: </label><br/>Animals<br/>Biopsy<br/>CCN Intercellular Signaling Proteins<br/>Case-Control Studies<br/>Cells, Cultured<br/>Disease Models, Animal<br/>Fibrillin-1<br/>Fibrillins<br/>Humans<br/>Intracellular Signaling Peptides and Proteins--metabolism<br/>Marfan Syndrome--metabolism<br/>Mice<br/>Mice, Mutant Strains<br/>Microfilament Proteins--antagonists & inhibitors<br/>Nephroblastoma Overexpressed Protein--metabolism<br/>Proto-Oncogene Proteins--metabolism<br/>Scleroderma, Systemic--metabolism<br/>Signal Transduction--physiology<br/>Skin--metabolism<br/>Smad3 Protein--metabolism<br/>Transforming Growth Factor beta--antagonists & inhibitors<br/>Wnt Proteins--antagonists & inhibitors