Huidekoper, Hidde H A potential role for muscle in glucose homeostasis: in vivo kinetic studies in glycogen storage disease type 1a and fructose-1,6-bisphosphatase deficiency. [electronic resource] - Journal of inherited metabolic disease Feb 2010 - 25-31 p. digital Publication Type: Case Reports; Journal Article ISSN: 1573-2665 Standard No.: 10.1007/s10545-009-9030-9 doi Subjects--Topical Terms: AdolescentBlood Glucose--metabolismFemaleFructose-1,6-Diphosphatase Deficiency--geneticsGluconeogenesisGlucose--metabolismGlycogen Storage Disease Type I--geneticsGlycogenolysisHomeostasisHumansHypoglycemia--geneticsKineticsLiver--metabolismMaleMuscles--metabolism