Mouse models for nuclear DNA-encoded mitochondrial complex I deficiency. [electronic resource]
- Journal of inherited metabolic disease Apr 2011
- 293-307 p. digital
Publication Type: Journal Article; Research Support, Non-U.S. Gov't; Review
1573-2665
10.1007/s10545-009-9005-x doi
Animals Cell Nucleus--genetics DNA--genetics DNA, Mitochondrial--genetics Disease Models, Animal Electron Transport Complex I--deficiency Humans Mice Mice, Knockout Mitochondrial Diseases--genetics Models, Biological Oxidative Phosphorylation Reactive Oxygen Species Treatment Outcome