TY - GEN AU - Goula,Agathi-Vassiliki AU - Berquist,Brian R AU - Wilson,David M AU - Wheeler,Vanessa C AU - Trottier,Yvon AU - Merienne,Karine TI - Stoichiometry of base excision repair proteins correlates with increased somatic CAG instability in striatum over cerebellum in Huntington's disease transgenic mice SN - 1553-7404 PY - 2010///0503 KW - Aging KW - metabolism KW - Animals KW - Base Sequence KW - Cerebellum KW - enzymology KW - DNA KW - chemistry KW - DNA Damage KW - DNA Glycosylases KW - DNA Polymerase beta KW - DNA Repair KW - genetics KW - DNA Repair Enzymes KW - DNA-(Apurinic or Apyrimidinic Site) Lyase KW - Flap Endonucleases KW - Genomic Instability KW - Huntington Disease KW - Mice KW - Mice, Transgenic KW - Models, Genetic KW - Molecular Sequence Data KW - Neostriatum KW - Nucleic Acid Conformation KW - Organ Specificity KW - Substrate Specificity KW - Trinucleotide Repeat Expansion N1 - Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, N.I.H., Intramural; Research Support, Non-U.S. Gov't UR - https://doi.org/10.1371/journal.pgen.1000749 ER -