Goula, Agathi-Vassiliki

Stoichiometry of base excision repair proteins correlates with increased somatic CAG instability in striatum over cerebellum in Huntington's disease transgenic mice. [electronic resource] - PLoS genetics Dec 2009 - e1000749 p. digital

Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, N.I.H., Intramural; Research Support, Non-U.S. Gov't

1553-7404

10.1371/journal.pgen.1000749 doi


Aging--metabolism
Animals
Base Sequence
Cerebellum--enzymology
DNA--chemistry
DNA Damage
DNA Glycosylases--metabolism
DNA Polymerase beta--metabolism
DNA Repair--genetics
DNA Repair Enzymes--genetics
DNA-(Apurinic or Apyrimidinic Site) Lyase--metabolism
Flap Endonucleases--metabolism
Genomic Instability--genetics
Huntington Disease--genetics
Mice
Mice, Transgenic
Models, Genetic
Molecular Sequence Data
Neostriatum--enzymology
Nucleic Acid Conformation
Organ Specificity--genetics
Substrate Specificity
Trinucleotide Repeat Expansion--genetics