Markert, M L
Purine nucleoside phosphorylase deficiency. [electronic resource]
- Immunodeficiency reviews 1991
- 45-81 p. digital
Publication Type: Case Reports; Journal Article; Research Support, Non-U.S. Gov't; Research Support, U.S. Gov't, P.H.S.; Review
0893-5300
B-Lymphocytes--immunology
Guanosine Triphosphate--metabolism
Humans
Models, Biological
Purine-Nucleoside Phosphorylase--deficiency
Purine-Pyrimidine Metabolism, Inborn Errors--immunology
Purines--metabolism
Pyrimidines--biosynthesis
Ribonucleotide Reductases
Severe Combined Immunodeficiency--etiology
T-Lymphocytes--drug effects
Tissue Distribution