Amritraj, Asha <br/><br/>
Increased activity and altered subcellular distribution of lysosomal enzymes determine neuronal vulnerability in Niemann-Pick type C1-deficient mice.  [electronic resource] 

 -  The American journal of pathology  Dec 2009 
 - 2540-56 p.  digital 
<br/><br/> Publication Type: Journal Article; Research Support, Non-U.S. Gov't 
<br/><br/><label>ISSN: </label>1525-2191 
<br/><br/><label>Standard No.: </label>10.2353/ajpath.2009.081096  doi 
<br/><br/><label>Subjects--Topical Terms: </label><br/>Animals<br/>Cathepsin B--metabolism<br/>Cathepsin D--metabolism<br/>Cerebellum--metabolism<br/>Cholesterol--metabolism<br/>Fluorescent Antibody Technique<br/>Hippocampus--metabolism<br/>Immunoblotting<br/>Intracellular Signaling Peptides and Proteins<br/>Lysosomes--enzymology<br/>Mice<br/>Mice, Inbred BALB C<br/>Mice, Knockout<br/>Microscopy, Electron, Transmission<br/>Nerve Degeneration--enzymology<br/>Neurons--enzymology<br/>Niemann-Pick C1 Protein<br/>Niemann-Pick Disease, Type C--enzymology<br/>Proteins--genetics