TY - GEN AU - Boy,Jana AU - Schmidt,Thorsten AU - Schumann,Ulrike AU - Grasshoff,Ute AU - Unser,Samy AU - Holzmann,Carsten AU - Schmitt,Ina AU - Karl,Tim AU - Laccone,Franco AU - Wolburg,Hartwig AU - Ibrahim,Saleh AU - Riess,Olaf TI - A transgenic mouse model of spinocerebellar ataxia type 3 resembling late disease onset and gender-specific instability of CAG repeats SN - 1095-953X PY - 2010///0615 KW - Age of Onset KW - Animals KW - Ataxin-3 KW - Brain KW - metabolism KW - Chromosomal Instability KW - genetics KW - Disease Models, Animal KW - Disease Progression KW - Gene Expression KW - Genetic Predisposition to Disease KW - Intranuclear Inclusion Bodies KW - Machado-Joseph Disease KW - Mice KW - Mice, Transgenic KW - Movement Disorders KW - Mutation KW - Nuclear Proteins KW - Rats KW - Sex Characteristics KW - Transcription Factors KW - Trinucleotide Repeats N1 - Publication Type: Journal Article; Research Support, Non-U.S. Gov't UR - https://doi.org/10.1016/j.nbd.2009.08.002 ER -