Kandert, Sebastian

Impaired nuclear functions lead to increased senescence and inefficient differentiation in human myoblasts with a dominant p.R545C mutation in the LMNA gene. [electronic resource] - European journal of cell biology Oct 2009 - 593-608 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

1618-1298

10.1016/j.ejcb.2009.06.002 doi


Aging--genetics
Amino Acid Substitution
Antibodies--metabolism
Bisbenzimidazole--metabolism
Carbocyanines--metabolism
Case-Control Studies
Cell Culture Techniques
Cell Differentiation--genetics
Cell Nucleus--metabolism
Cells, Cultured
Cysteine--metabolism
Female
Fluorescein-5-isothiocyanate--metabolism
Fluorescent Dyes--metabolism
Humans
Lamin Type A--genetics
Male
Muscular Dystrophy, Emery-Dreifuss--genetics
Mutation, Missense
Myoblasts--cytology
Point Mutation
Xanthenes--metabolism