TY  - GEN
AU  - Roumenina,Lubka T
AU  - Jablonski,Mathieu
AU  - Hue,Christophe
AU  - Blouin,Jacques
AU  - Dimitrov,Jordan D
AU  - Dragon-Durey,Marie-Agnes
AU  - Cayla,Mathieu
AU  - Fridman,Wolf H
AU  - Macher,Marie-Alice
AU  - Ribes,David
AU  - Moulonguet,Luc
AU  - Rostaing,Lionel
AU  - Satchell,Simon C
AU  - Mathieson,Peter W
AU  - Sautes-Fridman,Catherine
AU  - Loirat,Chantal
AU  - Regnier,Catherine H
AU  - Halbwachs-Mecarelli,Lise
AU  - Fremeaux-Bacchi,Veronique
TI  - Hyperfunctional C3 convertase leads to complement deposition on endothelial cells and contributes to atypical hemolytic uremic syndrome
SN  - 1528-0020
PY  - 2009///1027
KW  - Adolescent
KW  - Adult
KW  - Aged
KW  - Aged, 80 and over
KW  - Cells, Cultured
KW  - Child
KW  - Child, Preschool
KW  - Cohort Studies
KW  - Complement Activation
KW  - genetics
KW  - Complement C3-C5 Convertases
KW  - Complement System Proteins
KW  - Endothelial Cells
KW  - metabolism
KW  - Family
KW  - Female
KW  - Hemolytic-Uremic Syndrome
KW  - Humans
KW  - Infant
KW  - Infant, Newborn
KW  - Male
KW  - Middle Aged
KW  - Models, Molecular
KW  - Mutant Proteins
KW  - physiology
KW  - Pedigree
KW  - Young Adult
N1  - Publication Type: Journal Article; Research Support, Non-U.S. Gov't
UR  - https://doi.org/10.1182/blood-2009-01-197640
ER  -