TY - GEN AU - Srivastava,Sarika AU - Diaz,Francisca AU - Iommarini,Luisa AU - Aure,Karine AU - Lombes,Anne AU - Moraes,Carlos T TI - PGC-1alpha/beta induced expression partially compensates for respiratory chain defects in cells from patients with mitochondrial disorders SN - 1460-2083 PY - 2009///0714 KW - Carrier Proteins KW - genetics KW - Cell Respiration KW - Cells, Cultured KW - Child, Preschool KW - Electron Transport KW - Female KW - Fibroblasts KW - metabolism KW - Gene Expression KW - Heat-Shock Proteins KW - Humans KW - Infant KW - Male KW - Mitochondria KW - Mitochondrial Diseases KW - Peroxisome Proliferator-Activated Receptor Gamma Coactivator 1-alpha KW - RNA-Binding Proteins KW - Transcription Factors KW - Up-Regulation N1 - Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't UR - https://doi.org/10.1093/hmg/ddp093 ER -