Cytoplasmic retention of polyglutamine-expanded androgen receptor ameliorates disease via autophagy in a mouse model of spinal and bulbar muscular atrophy. [electronic resource]
- Human molecular genetics Jun 2009
- 1937-50 p. digital
Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't
1460-2083
10.1093/hmg/ddp115 doi
Androgens--metabolism Animals Autophagy Cell Line Cell Nucleus--genetics Cells, Cultured Cytoplasm--genetics Disease Models, Animal Humans Male Mice Mice, Transgenic Motor Activity Motor Neurons--cytology Muscular Atrophy, Spinal--genetics Nuclear Localization Signals--genetics Peptides--genetics Protein Transport Receptors, Androgen--genetics Trinucleotide Repeat Expansion