TY - GEN AU - Dobrowolny,Gabriella AU - Aucello,Michela AU - Rizzuto,Emanuele AU - Beccafico,Sara AU - Mammucari,Cristina AU - Boncompagni,Simona AU - Bonconpagni,Simona AU - Belia,Silvia AU - Wannenes,Francesca AU - Nicoletti,Carmine AU - Del Prete,Zaccaria AU - Rosenthal,Nadia AU - Molinaro,Mario AU - Protasi,Feliciano AU - Fanò,Giorgio AU - Sandri,Marco AU - Musarò,Antonio TI - Skeletal muscle is a primary target of SOD1G93A-mediated toxicity SN - 1932-7420 PY - 2009///0428 KW - Animals KW - Autophagy KW - physiology KW - Mice KW - Mice, Transgenic KW - Motor Neurons KW - metabolism KW - Muscle Contraction KW - Muscle, Skeletal KW - Muscular Atrophy KW - Mutation KW - Nerve Degeneration KW - pathology KW - Oxidative Stress KW - Reactive Oxygen Species KW - Sarcolemma KW - Spinal Cord KW - Superoxide Dismutase KW - genetics KW - Superoxide Dismutase-1 N1 - Publication Type: Journal Article; Research Support, Non-U.S. Gov't UR - https://doi.org/10.1016/j.cmet.2008.09.002 ER -