Emerick, Karan M Bile composition in Alagille Syndrome and PFIC patients having Partial External Biliary Diversion. [electronic resource] - BMC gastroenterology Oct 2008 - 47 p. digital Publication Type: Journal Article; Research Support, N.I.H., Extramural ISSN: 1471-230X Standard No.: 10.1186/1471-230X-8-47 doi Subjects--Topical Terms: AdolescentAlagille Syndrome--geneticsBile--metabolismBile Ducts, Intrahepatic--surgeryBiopsyChenodeoxycholic Acid--metabolismChildChild, PreschoolCholestasis, Intrahepatic--geneticsCholesterol--metabolismCholic Acid--metabolismDigestive System Surgical Procedures--methodsDisease ProgressionGallbladder--surgeryHumansInfantLipid Metabolism--physiologyLiver--pathologyPhospholipids--metabolismTreatment Outcome