Airway ion transport impacts on disease presentation and severity in cystic fibrosis. [electronic resource]
- Clinical biochemistry Jul 2008
- 764-72 p. digital
Publication Type: Journal Article; Multicenter Study; Research Support, Non-U.S. Gov't
1873-2933
10.1016/j.clinbiochem.2008.03.013 doi
Adolescent Adult Age Factors Biological Transport Child Child, Preschool Cystic Fibrosis--genetics Cystic Fibrosis Transmembrane Conductance Regulator--physiology Diseases in Twins Female Forced Expiratory Volume Humans Ion Transport--physiology Male Nasal Mucosa--physiopathology Perfusion Potentiometry Severity of Illness Index Siblings Sodium--metabolism