Zou, Yaqun

Muscle interstitial fibroblasts are the main source of collagen VI synthesis in skeletal muscle: implications for congenital muscular dystrophy types Ullrich and Bethlem. [electronic resource] - Journal of neuropathology and experimental neurology Feb 2008 - 144-54 p. digital

Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't

0022-3069

10.1097/nen.0b013e3181634ef7 doi


Animals
Animals, Newborn
Cell Differentiation--physiology
Cells, Cultured
Coculture Techniques--methods
Collagen Type VI--genetics
Fibroblasts--metabolism
Gene Expression Regulation--physiology
Humans
Mice
Mice, Inbred C57BL
Microscopy, Confocal--methods
Muscle, Skeletal--cytology
Muscular Dystrophies--pathology
Mutation
Skin--cytology