TY - GEN AU - Weimer,Jill M AU - Benedict,Jared W AU - Elshatory,Yasser M AU - Short,Douglas W AU - Ramirez-Montealegre,Denia AU - Ryan,Deborah A AU - Alexander,Noreen A AU - Federoff,Howard J AU - Cooper,Jonathan D AU - Pearce,David A TI - Alterations in striatal dopamine catabolism precede loss of substantia nigra neurons in a mouse model of juvenile neuronal ceroid lipofuscinosis SN - 0006-8993 PY - 2007///1019 KW - Age Factors KW - Analysis of Variance KW - Animals KW - Behavior, Animal KW - physiology KW - Catechol O-Methyltransferase KW - metabolism KW - Cell Death KW - genetics KW - Corpus Striatum KW - Disease Models, Animal KW - Dopamine KW - Gene Expression Regulation KW - Membrane Glycoproteins KW - deficiency KW - Mice KW - Mice, Knockout KW - Models, Biological KW - Molecular Chaperones KW - Motor Activity KW - Motor Skills KW - Neuronal Ceroid-Lipofuscinoses KW - Neurons KW - pathology KW - Substantia Nigra N1 - Publication Type: Journal Article; Research Support, N.I.H., Extramural UR - https://doi.org/10.1016/j.brainres.2007.05.018 ER -