Kuhn, Alexandre

Mutant huntingtin's effects on striatal gene expression in mice recapitulate changes observed in human Huntington's disease brain and do not differ with mutant huntingtin length or wild-type huntingtin dosage. [electronic resource] - Human molecular genetics Aug 2007 - 1845-61 p. digital

Publication Type: Comparative Study; Journal Article

0964-6906

10.1093/hmg/ddm133 doi


Animals
Brain--metabolism
Corpus Striatum--metabolism
Disease Models, Animal
Gene Dosage
Gene Expression
Humans
Huntingtin Protein
Huntington Disease--genetics
Mice
Mice, Mutant Strains
Mutation
Nerve Tissue Proteins--genetics
Neurons--metabolism
Nuclear Proteins--genetics
Phenotype
RNA, Messenger--metabolism