Weihl, Conrad C

Transgenic expression of inclusion body myopathy associated mutant p97/VCP causes weakness and ubiquitinated protein inclusions in mice. [electronic resource] - Human molecular genetics Apr 2007 - 919-28 p. digital

Publication Type: Journal Article; Research Support, N.I.H., Extramural

0964-6906

10.1093/hmg/ddm037 doi


Adenosine Triphosphatases--genetics
Animals
Cell Cycle Proteins--genetics
Gene Expression
Inclusion Bodies--metabolism
Mice
Mice, Inbred C57BL
Mice, Transgenic
Muscle Weakness--genetics
Muscle, Skeletal--metabolism
Mutant Proteins--genetics
Myositis, Inclusion Body--genetics
Organ Specificity
Proteasome Endopeptidase Complex--physiology
Sarcolemma--ultrastructure
Ubiquitin--metabolism
Valosin Containing Protein