TY  - GEN
AU  - Heare,T
AU  - Alp,N J
AU  - Priestman,D A
AU  - Kulkarni,A B
AU  - Qasba,P
AU  - Butters,T D
AU  - Dwek,R A
AU  - Clarke,K
AU  - Channon,K M
AU  - Platt,F M
TI  - Severe endothelial dysfunction in the aorta of a mouse model of Fabry disease; partial prevention by N-butyldeoxynojirimycin treatment
SN  - 1573-2665
PY  - 2007///0313
KW  - 1-Deoxynojirimycin
KW  - analogs & derivatives
KW  - Animals
KW  - Aorta
KW  - drug effects
KW  - Disease Models, Animal
KW  - Enzyme Inhibitors
KW  - therapeutic use
KW  - Fabry Disease
KW  - drug therapy
KW  - Female
KW  - Humans
KW  - Male
KW  - Mice
KW  - Mice, Inbred C57BL
KW  - Mice, Knockout
KW  - Microscopy, Electron
KW  - Phenotype
KW  - alpha-Galactosidase
KW  - genetics
N1  - Publication Type: Journal Article; Research Support, Non-U.S. Gov't
UR  - https://doi.org/10.1007/s10545-006-0473-y
ER  -