Heare, T <br/><br/>
Severe endothelial dysfunction in the aorta of a mouse model of Fabry disease; partial prevention by N-butyldeoxynojirimycin treatment.  [electronic resource] 

 -  Journal of inherited metabolic disease  Feb 2007 
 - 79-87 p.  digital 
<br/><br/> Publication Type: Journal Article; Research Support, Non-U.S. Gov't 
<br/><br/><label>ISSN: </label>1573-2665 
<br/><br/><label>Standard No.: </label>10.1007/s10545-006-0473-y  doi 
<br/><br/><label>Subjects--Topical Terms: </label><br/>1-Deoxynojirimycin--analogs & derivatives<br/>Animals<br/>Aorta--drug effects<br/>Disease Models, Animal<br/>Enzyme Inhibitors--therapeutic use<br/>Fabry Disease--drug therapy<br/>Female<br/>Humans<br/>Male<br/>Mice<br/>Mice, Inbred C57BL<br/>Mice, Knockout<br/>Microscopy, Electron<br/>Phenotype<br/>alpha-Galactosidase--genetics