Meola, G
[Expression of a defect in the respiratory chain in cultured human cells]. [electronic resource]
- Rivista di neurologia
- 122-34 p. digital
Publication Type: English Abstract; Journal Article
0035-6344
Blotting, Southern
Cells, Cultured
Chromosome Deletion
Cytochrome-c Oxidase Deficiency
DNA--genetics
DNA, Mitochondrial--genetics
Electron Transport
Electron Transport Complex IV--genetics
Fibroblasts--pathology
Gene Expression Regulation
Humans
Mitochondria, Muscle--enzymology
Models, Chemical
Muscle Proteins--deficiency
Muscles--enzymology
NADH Dehydrogenase--genetics
Ophthalmoplegia--enzymology
Oxidative Phosphorylation Coupling Factors--genetics
Polymerase Chain Reaction
Proton-Translocating ATPases--genetics