Meola, G

[Expression of a defect in the respiratory chain in cultured human cells]. [electronic resource] - Rivista di neurologia - 122-34 p. digital

Publication Type: English Abstract; Journal Article

0035-6344


Blotting, Southern
Cells, Cultured
Chromosome Deletion
Cytochrome-c Oxidase Deficiency
DNA--genetics
DNA, Mitochondrial--genetics
Electron Transport
Electron Transport Complex IV--genetics
Fibroblasts--pathology
Gene Expression Regulation
Humans
Mitochondria, Muscle--enzymology
Models, Chemical
Muscle Proteins--deficiency
Muscles--enzymology
NADH Dehydrogenase--genetics
Ophthalmoplegia--enzymology
Oxidative Phosphorylation Coupling Factors--genetics
Polymerase Chain Reaction
Proton-Translocating ATPases--genetics