TY - GEN AU - Rocha,Luiz Otávio Savassi AU - Quirino,Beatriz Eugênia Gomes AU - Melo,Frederico Henrique Corrêa de AU - Leite,Virgínia Hora Rios AU - Godoy,Pérsio AU - Valadares,Eugênia Ribeiro TI - [Case 3/2006--progressive respiratory failure in a 33 year-old man with heart disease and remarkable somatic dysmorphism] SN - 0066-782X PY - 2007///0329 KW - Adult KW - Aortic Valve Insufficiency KW - complications KW - Bronchopneumonia KW - pathology KW - Echocardiography, Doppler, Color KW - Electrophoresis KW - Fatal Outcome KW - Heart Diseases KW - Humans KW - Male KW - Mucopolysaccharidoses KW - Myocardium KW - ultrastructure KW - Respiratory Insufficiency KW - etiology N1 - Publication Type: Case Reports; Clinical Conference; Journal Article UR - https://doi.org/10.1590/s0066-782x2006001400010 ER -