Lee, Jeong Woong

Editing-defective tRNA synthetase causes protein misfolding and neurodegeneration. [electronic resource] - Nature Sep 2006 - 50-5 p. digital

Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't

1476-4687

10.1038/nature05096 doi


Acetylation
Alanine--genetics
Alanine-tRNA Ligase--chemistry
Animals
Catalysis
Escherichia coli--genetics
Fibroblasts
Humans
Mice
Mice, Inbred C57BL
Mice, Mutant Strains
Models, Molecular
Molecular Sequence Data
Mutation--genetics
Neurodegenerative Diseases--enzymology
Phenotype
Protein Folding
Protein Structure, Tertiary
Purkinje Cells--metabolism
RNA, Transfer, Ala--genetics
Serine--genetics