Tenascin-C is induced by mutated BMP type II receptors in familial forms of pulmonary arterial hypertension. [electronic resource]
- American journal of physiology. Lung cellular and molecular physiology Oct 2006
- L694-702 p. digital
Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't
1040-0605
10.1152/ajplung.00119.2006 doi
Bone Morphogenetic Protein Receptors--antagonists & inhibitors Bone Morphogenetic Protein Receptors, Type II--genetics Cells, Cultured Extracellular Signal-Regulated MAP Kinases--metabolism Homeodomain Proteins--metabolism Humans Hypertension, Pulmonary--genetics Mutation Myocytes, Smooth Muscle--metabolism Pulmonary Artery--metabolism Signal Transduction Smad Proteins, Receptor-Regulated--metabolism Tenascin--biosynthesis