TY - GEN AU - Janssen,Antoon J M AU - Trijbels,Frans J M AU - Sengers,Rob C A AU - Wintjes,Liesbeth T M AU - Ruitenbeek,Wim AU - Smeitink,Jan A M AU - Morava,Eva AU - van Engelen,Baziel G M AU - van den Heuvel,Lambert P AU - Rodenburg,Richard J T TI - Measurement of the energy-generating capacity of human muscle mitochondria: diagnostic procedure and application to human pathology SN - 0009-9147 PY - 2006///0619 KW - Adenosine Triphosphate KW - biosynthesis KW - Adolescent KW - Adult KW - Biopsy KW - Carbon Radioisotopes KW - Carnitine KW - metabolism KW - Child KW - Child, Preschool KW - Energy Metabolism KW - Female KW - Humans KW - Malates KW - Male KW - Malonates KW - Mitochondria KW - Mitochondrial ADP, ATP Translocases KW - deficiency KW - Mitochondrial Diseases KW - diagnosis KW - Muscle, Skeletal KW - Oxidation-Reduction KW - Oxidative Phosphorylation KW - Pyruvate Dehydrogenase Complex KW - Pyruvic Acid KW - Succinic Acid N1 - Publication Type: Journal Article UR - https://doi.org/10.1373/clinchem.2005.062414 ER -