Janssen, Antoon J M Measurement of the energy-generating capacity of human muscle mitochondria: diagnostic procedure and application to human pathology. [electronic resource] - Clinical chemistry May 2006 - 860-71 p. digital Publication Type: Journal Article ISSN: 0009-9147 Standard No.: 10.1373/clinchem.2005.062414 doi Subjects--Topical Terms: Adenosine Triphosphate--biosynthesisAdolescentAdultBiopsyCarbon RadioisotopesCarnitine--metabolismChildChild, PreschoolEnergy MetabolismFemaleHumansMalates--metabolismMaleMalonates--metabolismMitochondria--metabolismMitochondrial ADP, ATP Translocases--deficiencyMitochondrial Diseases--diagnosisMuscle, Skeletal--metabolismOxidation-ReductionOxidative PhosphorylationPyruvate Dehydrogenase Complex--metabolismPyruvic Acid--metabolismSuccinic Acid--metabolism