Van Goor, Fredrick

Rescue of DeltaF508-CFTR trafficking and gating in human cystic fibrosis airway primary cultures by small molecules. [electronic resource] - American journal of physiology. Lung cellular and molecular physiology Jun 2006 - L1117-30 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

1040-0605

10.1152/ajplung.00169.2005 doi


3T3 Cells
Animals
Biotinylation
Cell Line
Cells, Cultured
Chlorides--metabolism
Cresols--metabolism
Cystic Fibrosis--genetics
Cystic Fibrosis Transmembrane Conductance Regulator--genetics
Humans
Ion Channel Gating
Mice
Pyrazoles--metabolism
Rats
Recombinant Proteins--metabolism
Sequence Deletion
Thyroid Gland--physiology