Chromogranin-mediated secretion of mutant superoxide dismutase proteins linked to amyotrophic lateral sclerosis. [electronic resource]
- Nature neuroscience Jan 2006
- 108-18 p. digital
Publication Type: Journal Article; Research Support, Non-U.S. Gov't
1097-6256
10.1038/nn1603 doi
3T3 Cells Amyotrophic Lateral Sclerosis--enzymology Animals Astrocytes--metabolism Blotting, Western COS Cells Cells, Cultured Chlorocebus aethiops Chromogranin A Chromogranins--physiology Fluorescent Antibody Technique Gliosis--pathology Humans Immunoprecipitation Interneurons--metabolism Mice Mice, Transgenic Microscopy, Immunoelectron Microsomes--enzymology Molecular Chaperones--genetics Motor Neurons--metabolism Mutation--physiology Plasmids--genetics Proteasome Inhibitors Protein Folding Spinal Cord--cytology Subcellular Fractions--physiology Superoxide Dismutase--genetics Superoxide Dismutase-1