Maloyan, Alina

Mitochondrial dysfunction and apoptosis underlie the pathogenic process in alpha-B-crystallin desmin-related cardiomyopathy. [electronic resource] - Circulation Nov 2005 - 3451-61 p. digital

Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't

1524-4539

10.1161/CIRCULATIONAHA.105.572552 doi


Amyloid
Animals
Apoptosis
Cardiomyopathies--etiology
Cells, Cultured
Desmin--physiology
Dimerization
Humans
Ion Channels
Mice
Mice, Transgenic
Mitochondrial Diseases--complications
Mitochondrial Membrane Transport Proteins
Mitochondrial Permeability Transition Pore
Mutation, Missense
Myocardial Contraction
Myocytes, Cardiac--cytology
Rats
Transfection
alpha-Crystallin B Chain--genetics